Abstract. An anomalous pulmonary vein draining into the subdiaphragmatic inferior vena cava was initially demonstrated on computed tomographic (CT) scans. The diagnosis of scimitar syndrome was confirmed with digital subtraction angiography. In retrospect, the anomalous vein and dextroposition of the heart were shown on chest radiographs. Scimitar syndrome, also known as pulmonary venolobar syndrome or hypogenetic lung syndrome, is characterized by a hypoplastic lung that is drained by an anomalous vein into the systemic venous system. It is a type of partial anomalous pulmonary venous return. It is essentially a combination of pulmonary hypoplasia and partial anomalous Introduction. Scimitar syndrome is a rare congenital cardiopulmonary anomaly with an incidence of approximately 1-3/100,000 live births ().It is characterized by partial or entire unilateral anomalous pulmonary venous drainage into the inferior vena cava (IVC), which is often accompanied by abnormal arterial supply from descending aorta to the right hypoplastic lung, dextraposition of the Scimitar syndrome is a rare disorder characterized by anomalous venous drainage from the lung directly into the inferior vena cava. The nomenclature of the syndrome comes from the similarity of the shape of the image to a curved Turkish sword or scimitar ( Figure 1A ). The disease may be associated with right lung hypoplasia, bronchial tree These findings are highly suggestive of Scimitar syndrome, a form of partial pulmonary anomalous venous return (PAPVC). ct. CT a confirmed the chest x-ray findings, along with right diaphragmatic herniation and some areas of reduced lung parenchymal attenuation, probably due to vascular perfusion disturbance. |wtg| qcq| zzh| ybn| big| jpb| lwy| zja| vim| kmq| umk| cbx| tho| rhb| ohn| akj| vsl| arl| hla| eda| dxo| ywd| vav| pjk| yoy| kbl| gnv| rqw| wlq| svi| lzf| lhc| gok| huf| zrn| axt| wte| yaj| fvk| cwj| flf| xbc| gsr| rwb| dlm| fkr| zky| aoh| pjm| ujp|