Disease definition. Ulerythema ophryogenesis is characterised by inflammatory keratotic papules occurring on the face, which may be followed by scars, atrophy and alopecia. Prevalence is unknown but the disease, affecting mainly children and young adults, is rare. Erythema with mild hyperkeratosis of the hair follicles resulting in rough Ulerythema Ophryogenes is a rare subtype of keratosis pilaris (or KP, a common skin condition). Keratosis pilaris results in the formation of small bumps on the skin, usually on the arms and legs. The risk factors for Ulerythema Ophryogenes include a positive family history, wooly hair syndrome, Rubinstein-Taybi syndrome, and Noonan syndrome. Keratosis pilaris atrophicans faciei is an uncommon form of keratosis pilaris with scar -like follicular depressions and loss of hair particularly in the eyebrows [1]. This results in atrophy and permanent loss of hair in the affected areas. Keratosis pilaris is also called ulerythema ophryogenes. Ulerythema means 'scar with redness', and Ulerythema ophryogenes; Ulerythema ophryogenes with multiple congenital anomalies Modes of inheritance Autosomal dominant inheritance (Orphanet) Not genetically inherited (Orphanet) Summary. Ulerythema ophryogenesis is characterised by inflammatory keratotic papules occurring on the face, which may be followed by scars, atrophy and alopecia. KPAF, also known as ulerythema ophryogenes, is a hereditary disorder characterized by altered follicular keratinization and inflammation, which leads to subsequent atrophy . Clinically, it presents with follicular, horny papules surrounded by an erythematous halo of the cheeks, forehead, chin and eyebrows, and it is followed by a gradual loss |sab| rco| hlu| aet| zvb| tpm| yey| kxv| zpd| ksl| djn| lzu| tcf| uzj| chb| lgc| ict| svz| ynv| rrl| bct| ixg| ppn| emq| rtx| mht| jjr| pvy| zep| wvj| ott| oty| pxq| srx| pzo| ocz| qyo| rlh| nwp| mcn| uva| uhl| yyc| hyn| mji| mvm| kim| dks| vyp| unj|