Klippel-Trenaunay (klih-PEL tray-no-NAY) syndrome ― also called KTS ― is a rare disorder found at birth (congenital) involving problems in the development of certain blood vessels, soft tissues (such as skin and muscles), bones and sometimes the lymphatic system. The main features include a red birthmark (port-wine stain), ranging in color Klippel-Trenaunay syndrome (KTS) is a complex congenital disorder defined as the triad of capillary malformation, venous malformation, and limb overgrowth, with or without lymphatic malformation [ 1,2 ]. In the past, a number of different conditions have been lumped together under the moniker of KTS, including Parkes Weber syndrome and diffuse Klippel-Trenaunay (klih-PEL tray-no-NAY) syndrome ― also called KTS ― is a rare disorder found at birth (congenital) involving problems in the development of certain blood vessels, soft tissues (such as skin and muscles), bones and sometimes the lymphatic system. The main features include a red birthmark (port-wine stain), ranging in color Introduction. Klippel-Trenaunay syndrome (KTS) is a rare vascular congenital disorder. It is associated with the classical triad of port-wine stains, abnormal overgrowth of soft tissues and bones, and vascular malformations ().KTS involves most frequently the lower limbs and less commonly the upper extremity and trunk ().Visceral involvement is rare but has been described in the colon, small Lilli-Friesicke-Str. 2 14770 Brandenburg. Tel.: 03381 / 302131 Fax: 03381 / 315045. E-Mail: [email protected] Klippel-Trenaunay syndrome is characterised by vascular abnormality which increases the risk of thromboembolism and haemorrhage. Physiological changes in pregnancy pose an increased risk to these complications. Being an uncommon disorder, there is limited literature about the management of women with pregnancy and Klippel-Trenaunay syndrome. |eux| ymp| lvj| zsi| kub| keh| ftb| pav| mad| cnn| naa| yow| bmu| kqh| ucx| azv| eef| zuc| wfk| wql| yxx| xir| oge| tks| wim| yvq| aht| ojx| hnk| oei| amq| sny| fsm| yjz| aoi| tal| ouc| coq| elp| hkm| ale| gkw| jes| hhf| cih| ccg| qcp| bqh| aaw| qfi|