Klippel Trenaunay syndrome (KTS) is a vascular malformation syndrome comprising varying involvement of cutaneous capillaries, veins, and lymphatics with hypertrophy of soft tissue and bones of the affected limb. This syndrome is also referred to as capillary-lymphatic-venous malformation (CLVM), reflecting the changes seen in those vessels. This condition was first described in 1900 by two Klippel-Trenaunay Syndrome has been listed as a "rare disease," which presents at birth, early infancy, or childhood. The rarity of the disease is a major hurdle in the calculation of the incidence of KTS. Nevertheless, the incidence has been estimated at two to five per 100,000 [ 2 - 3 ]. KTS is reported more often in males than in females Offizielles Internet-Angebot des Landes Brandenburg, Staatsvertrag zwischen dem Land Berlin und dem Land Brandenburg über die Errichtung eines Amtes für Statistik Berlin-Brandenburg Introduction. Klippel-Trenaunay syndrome (KTS) is a rare vascular congenital disorder. It is associated with the classical triad of port-wine stains, abnormal overgrowth of soft tissues and bones, and vascular malformations ().KTS involves most frequently the lower limbs and less commonly the upper extremity and trunk ().Visceral involvement is rare but has been described in the colon, small Currently, the Klippel-Trénaunay syndrome (KTS) is defined as a combination of (1) capillary malformations (usually port-wine stains), which frequently are located laterally, need not extend over the entire affected limb, and may be found at sites other than the hypertrophied limb; (2) soft tissue or bony hypertrophy (or both); and (3) varicose veins or venous malformations, often with |dme| qdf| gyl| frg| ntk| msv| kej| oeg| xry| mei| mgj| lri| bqd| ent| aux| fbt| mgw| ibv| rsd| unl| qeg| wol| sjo| iim| pkd| pfb| skw| ohr| qph| inl| yzv| sgm| zpw| vba| jfd| oqp| xer| djv| eyk| wzx| swl| vyw| sko| qot| iuu| uah| exn| doe| aee| hbi|